Seizures in infancy are common. Although there are a number of clearly defined epilepsy syndromes which begin or occur in infancy many infants cannot be readily classified into currently recognised epilepsy syndromes. This review discusses the clinical presentation, EEG findings, natural history and management of several recognisable epilepsy syndromes in infancy. Special syndromes including febrile convulsions and symptomatic seizures are discussed. There is also advice about investigation of seizures and syndromes in this population.